Reversal of cardiomyopathy in propionic acidemia after liver transplantation: a 10-year follow-up
نویسندگان
چکیده
منابع مشابه
Intractable metabolic acidosis in a child with propionic acidemia undergoing liver transplantation -a case report-
Propionic acidemia (PA) is a rare autosomal recessive disorder of metabolism caused by deficient activity of the mitochondrial enzyme propionyl-CoA carboxylase. The clinical manifestations are metabolic acidosis, poor feeding, lethargy, vomiting, osteoporosis, neurological dysfunction, pancytopenia, developmental retardation and cardiomyopathy. Liver transplantation has recently been considered...
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Islet transplantation can restore endogenous beta-cell function to subjects with type 1 diabetes. Sixty-five patients received an islet transplant in Edmonton as of 1 November 2004. Their mean age was 42.9 +/- 1.2 years, their mean duration of diabetes was 27.1 +/- 1.3 years, and 57% were women. The main indication was problematic hypoglycemia. Forty-four patients completed the islet transplant...
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In 1988, Ludwig et al proposed the term idiopathic adulthood ductopenia (IAD) for the condition of chronic cholestatic liver disease associated with loss of intrahepatic bile ducts of unknown etiology with clinical onset in adulthood (1). In recent years, several cases of idiopathic biliary ductopenia in adulthood have been described. This disease is severe in most cases and can progress to cir...
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ژورنال
عنوان ژورنال: Transplant International
سال: 2015
ISSN: 0934-0874
DOI: 10.1111/tri.12677